Sjældne sygdomme

1p36 deletionssyndrom

16p11.2 deletionssyndrom

18q deletion syndrom

22q11 deletion-syndrom

3M syndrom

7q11.23 duplikationssyndrom

Abetalipoproteinæmi

Adrenogenitalt syndrom

Adrenoleukodystrofi

Aicardi-Goutières' syndrom

Aicardi syndrom

Akondroplasi

Alagilles syndrom

Albrights hereditære osteodystrofi

Alexanders sygdom

Alfa-1 antitrypsinmangel

Alports syndrom

Alströms syndrom

Alternerende hemiplegi

Androgen insensitivitetssyndrom

Angelmans syndrom

Aperts syndrom

Aplasia cutis congenita

Argininoravsyreæmi

Arthrogryposis multiplex congenita

Ashermans syndrom

Ataxia telangiektasia

ATRX syndrom

Bannayan-Riley-Ruvalcabas syndrom

Barraquer-Simons' syndrom

Bartter syndrom

Beckwith-Wiedemanns syndrom

Behrs syndrom

Biotinidase mangel

Birt-Hogg-Dube syndrom

Blæreekstrofi/epispadi

Blue rubber bleb nævus

Bohring-Opitz' syndrom

CADASIL

Caffey syndrom

Campomel dysplasi

Canavans syndrom

Carnitin transporter defekt

Carpenters syndrom

CDG syndrom - Congenital disorders of glycosylation

CHARGE-syndrom

Chondrodysplasia punctata

Citrullinæmi

Cleidocranial dysplasia

CLOVES syndrom

Cockaynes syndrom

Coffin-Lowrys syndrom

Coffin-Siris' syndrom

Cohen syndrom

Congenital contractural arachnodactyly

Cornelia de Langes syndrom

Costellos syndrom

Cranium bifidum

Cri du chat syndrom

Crouzon syndrom

Cutis marmorata telangiectatica congenita

Cystinose

Cystinuri

Dandy-Walkers syndrom

Dariers sygdom

Dercums sygdom

Diamond-Blackfans syndrom

Diastrofisk dysplasi

Duane-radial ray syndrom

Dubowitz' syndrom

Dyggve-Melchior-Clausens syndrom

Ektrodaktyli, Ektodermal dysplasi og læbe-gane-spalte

Ellis-van Creveld

Emanuels syndrom

Epidermolysis bullosa

Fabrys sygdom

Fanconis anæmi

Fenylketonuri

FG syndrom

Fibrodysplasia ossificans progressiva

Fibrøs dysplasi

Fiskelugt syndromet

Floating Harbor syndrom

Fragilt X-syndrom

Freeman-Sheldon syndrom

Friedreichs ataksi

Fukosidose

Fumarase mangel

Galaktosæmi

Gauchers sygdom

Gillespies syndrom

Glukose transporter type 1 defekt

Glutaraciduri type 1

Glutaraciduri type 3

Glykogenose type 1

Goldenhars syndrom

Gomez-Lopez-Hernandez syndrom

Gorlins syndrom

Greigs cefalopolysyndaktyli

Greigs syndrom

Hallermann-Streiff syndrom

Hartnup sygdom

Hemihyperplasi (isoleret)

Hereditært angioødem

Hereditær trykbetinget neuropati

Holoprosencefali

Holt-Orams syndrom

Homocystinuri

Hunters syndrom

Huntingtons sygdom

Hurler-Scheie syndrom

Hurler syndrom

Hyper-IgD syndrom

Hypofosfatasi

Hypohidrotisk ectodermal dysplasi

Incontinentia pigmenti

Isovalerianesyreæmi

Jacobsens syndrom

Jeunes syndrom

Jobs syndrom

Jouberts syndrom

Kabuki-syndrom

Kallmanns syndrom

Karbamylfosfat syntase defekt

Kardiofaciokutane syndrom

Kaudalt regressionssyndrom

KBG syndrom

Kearns-Sayres syndrom

Kindlers syndrom

Kleefstras syndrom

Klinefelters syndrom

Klippel-Feils syndrom

Klippel-Trénaunays syndrom

Kløverbladskranium

Kongenit central hypoventilationssyndrom

Koolen-de Vries' syndrom

Krabbes sygdom

Kromosom 9p deletionssyndrom

Kufs sygdom

Lamellær ichthyosis

Langkædet 3-hydroxy-acyl-CoA dehydrogenase mangel

Larsen syndrom

Lebers hereditære optikus neuropati

Leighs syndrom

Lesch-Nyhans syndrom

Loeys-dietz' syndrom

Lowes syndrom

Lysosomale sygdomme

Machado-Joseph sygdom

Madelung-deformitet

Maffuccis syndrom

Mannosidose

Maple syrup urine disease (Ahornsirup-urin sygdom)

Marfans syndrom

Maroteux-Lamys syndrom

MASA

McArdles sygdom

McCune-Albright syndrom

MECP2 duplikationssyndrom

MED13L-relateret udviklingshæmning

Medfødte multiple eksostoser

Megaloencefal leukoencefalopati med subkortikale cyster

Meget langkædet acyl-CoA dehydrogenase mangel

MELAS

Mellemkædet acyl-CoA dehydrogenase defekt

Melnick-Needles syndrom

Menkes sygdom

MERRF

Metafysær kondrodysplasi, type Jansen

Metakondromatose

Metakromatisk leukodystrofi

Metylkrotonyl-CoA karboxylase mangel

Methylentetrahydrofolat reduktase defekt

Metylglutakonsyreæmi

Methylmalonsyreæmi

Mikrocefal osteodysplastisk primordial dværgvækst type 1

Mikrocefal osteodysplastisk primordial dværgvækst type 2

Milroy sygdom

Mitokondriesygdomme

Mohr-Tranebjærgs syndrom

Morquios sygdom

Mowat-Wilson syndrom

Muckle-Wells syndrom

Muenkes syndrom

Mukolipidoser

Mukopolysakkaridoser

Multipel epifysedysplasi

Multipel karboxylase mangel

Multipel sulfatasemangel

Möbius' syndrom

Negl-patella syndrom

Neuralrørsdefekter

Neurofibromatose type 1

Neurofibromatose type 2

Neuromyelitis optica - Devics sygdom

Nievergelts syndrom

Nonketotisk hypeglycinæmi

Noonans syndrom

Norries sygdom

Okulodentodigital dysplasi

Okulokutan albinisme

Okulær albinisme

Olliers syndrom

Opitz G/BBB syndrom

Ornithin transkarbamylase defekt

Orofaciodigitalt syndrom type 1

Osteogenesis imperfecta

Osteopathia stratia with cranial sclerosis (OSCS)

Osteopetrose

Pallister-Halls syndrom

Pallister-Killian syndrom

PANDAS/PANS

Parry-Rombergs syndrom

Pataus syndrom

Pearsons syndrome

Pelizaeus-Merzbachers sygdom

Pena-Shokeirs syndrom, type 1

Pendred syndrom

Peroxisomal biogenese sygdomme

Peutz-Jeghers syndrom

PHACE-syndrom (PHACES-syndrom)

Phelan-McDermids syndrom

Pierre Robin-sekvens

Pitt-Hopkins syndrom

Polands syndrom

Pompes sygdom

Pontocerebellar hypoplasi type 2

Potocki-Lupskis syndrom

Prader-Willi syndrom

Primær hyperoxaluri type 1

Progeria

Proksimal fokal femurdefekt

Prolidase defekt

Propionsyreæmi

Proteus syndrom

Prune belly syndrom

Pseudoxanthoma elasticum

Pyknodysostose

Pyruvat dehydrogenase mangel

Pyruvatkinase mangel

Refsums sygdom

Respirationskædedefekter (Kompleks I-V defekter)

Retts syndrom

Ritscher-Schinzels syndrom

Robinows syndrom

Rothmund-Thomsons syndrom

Rubinstein-Taybi syndrom

Sallas sygdom

Sandhoffs sygdom

Sanfilippos syndrom

Scheies syndrom

Schwannomatose

Seckels syndrom

Septooptisk dysplasi

Shprintzen-Goldberg syndrom

Shwachman-Diamond syndrom

Silver-Russell syndrom

Simpson-Golabi-Behmel syndrom

Slys syndrom

Smith-Lemli-Opitz' syndrom

Smith-Magenis syndrom

Sneddon syndrom

Sotos' syndrom

Spielmeyer-Vogts syndrom

Spinal muskelatrofi

Spondyloepifysær dysplasi

Stargardts sygdom

Sticklers syndrom

Stiff person syndrom

Sturge-Webers syndrom

Sulfitoxidase mangel

Susacs syndrom

TAR syndrom

Tay-Sachs' sygdom

Thanatofor dysplasi

Tibial aplasia ectrodactyli

Treacher Collins' syndrom

Trichorhinophalangealt syndrom type 1

Trichorhinophalangeal syndrom type II

Trisomi 14 mosaik

Trisomi 18, Edwards' syndrom

Tuberøs sklerose

Turners syndrom

Tyrosinæmi type 1

Tyrosinæmi type 2

Urinstofcyklusdefekter

Unverricht-Lundborg sygdom

Ushers syndrom

VACTERL

Vaskulær Ehlers-Danlos' syndrom

Von Hippel-Lindaus sygdom

Waardenburg syndrom type 1

WAGR syndrom

Walker-Warburgs syndrom

Wiedemann-Steiners syndrom

Wildervanck syndrome

Williams' syndrom

Wolf-Hirschhorn syndrom

Wolframs syndrom

X-bunden hypofosfatæmisk rakitis

Xeroderma pigmentosum

Yellow-Nail syndrom

Aagenæs' syndrom

Aarskogs syndrom